Multiple choice The four pulmonary veins become malpositioned in Shone's syndrome Pentalogy of cantrell Tetralogy of fallot Total anomalous pulmonary venous connection (TAPVC) Reveal answer Fill a bubble to check yourself D Correct answer Explanation Total anomalous pulmonary venous connection (TAPVC), is a rare cyanotic congenital heart defect (CHD) in which all four pulmonary veins are malpositioned and make anomalous connections to the systemic venous circulation.